Lysine 2 Oxoglutarate Dioxygenase

Medical Condition:
Lysine 2 Oxoglutarate Dioxygenase

A mixed-function oxygenase that catalyzes the hydroxylation of peptidyllysine, usually in protocollagen, to peptidylhydroxylysine. The enzyme utilizes molecular oxygen with concomitant oxidative decarboxylation of the cosubstrate 2-oxoglutarate to succinate. EC 1.14.11.4.