Acetohydroxyacid Synthetase I

Medical Condition:
Acetohydroxyacid Synthetase I

A flavoprotein that catalyzes the formation of acetolactate from 2 moles of pyruvate in the biosynthesis of valine and the formation of acetohydroxybutyrate from pyruvate and alpha-ketobutyrate in the biosynthesis of isoleucine. EC 4.1.3.18.